Disclaimer: This toolkit is intended to provide resources for school nursing practice as it relates to the care of students with Bleeding Disorders in Oregon schools. This is not medical nor nurse practice advice and is not prescriptive as it relates to individual students or individual nursing practice. These resources do not override individual assessment, and clinical judgement. Nurses are responsible for their own assessment and practice.
Bleeding disorders are a group of conditions resulting in improper blood clotting. These conditions can be acquired or inherited and are characterized by a lack of clotting factors in the blood. The severity of a bleeding disorder is determined by the amount of the deficient clotting factor in the blood, ranging from mild to severe (American Society of Hematology [ASH], 2023).
Hemophilia, while probably the most well known bleeding disorder, is relatively rare and mostly affects males. The most common inherited bleeding disorder is von Willebrand Disease, which can affect both biological males and females (ASH, 2023).
Bleeding disorders can also be acquired, caused by a disease or medication (ASH, 2023). Diseases and conditions that can cause bleeding disorders include pregnancy, cancer, multiple sclerosis, and autoimmune conditions (Mayo Clinic, 2021). Examples of acquired bleeding disorders include Disseminated Intravascular Coagulation (DIC), vitamin K deficiency bleeding, liver disease associated bleeding, and arteriovenous malformations, along with deficiencies of certain clotting factors, named for the deficient factor (ASH, 2023).
It is important that school staff provide reasonable protection for all students. Treatment, response, and considerations for students with bleeding disorders while at school should address:
- Basic first aid with use of universal precautions
- Bleeding symptoms, especially bleeding into joints or the brain
- Appropriate response after serious injury or with symptoms of bleeding
- Accommodation considerations, i.e. physical education, field trips, extended absences, 504 or IEP
- Self-Management
- Absenteeism and Academic impact
- Psychosocial Implications of chronic disease
(Steps for Living, 2020; Schrijvers, Schuurmans & Fischer, 2016; Shapiro et al, 2001; Cyagan, Maier & O’Neill, 2012)
Evidence Based Practice
Literature Review
Basic Disease Information
Legal Practice Standards
At the forefront of nurse case management for school nurses, is the understanding of scope of practice as it relates to case management and delegation of nursing tasks in a community setting:
Public Access Resources
Note: the following are national or regional resources that serve as a reference, they may or may not be consistent with Oregon law and do not supersede Oregon Nurse Practice.
Hemophilia Federation of America
National Hemophilia Foundation
School Nursing 101
Centers for Disease Control and Prevention(CDC)
National Hemophilia Foundation
Professional Development
NIH
- Haider MZ, Anwer F. Acquired Hemophilia. [Updated 2022 Sep 26]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK560494/
- Doherty TM, Kelley A. Bleeding Disorders. [Updated 2022 May 8]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK541050/
- Stoj KM, Pierro J. Factor V Deficiency. [Updated 2022 Mar 19]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK580494/
- Mangla A, Hamad H, Kumar A. Factor XIII Deficiency. [Updated 2022 Nov 30]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK557467/
- Mehta P, Reddivari AKR. Hemophilia. [Updated 2022 Sep 30]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK551607/
- Salen P, Babiker HM. Hemophilia A. [Updated 2023 Feb 5]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK470265/
- Alshaikhli A, Rokkam VR. Hemophilia B. [Updated 2022 Oct 19]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK560792/
- Sabih A, Babiker HM. Von Willebrand Disease. [Updated 2022 Aug 29]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2022 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK459222/
- Broussard IM, Kahwaji CI. Universal Precautions. [Updated 2023 Jul 29]. In: StatPearls [Internet]. Treasure Island (FL): StatPearls Publishing; 2023 Jan-. Available from: https://www.ncbi.nlm.nih.gov/books/NBK470223/
STATPEARLS CE
CDC
National Hemophilia Foundation
Hemostasis and Thrombosis Resource Center
Osmosis
Learning in Ten (LIT)
UAP Training Resources
In the state of Oregon there are specific training required for care of students with diabetes that are prerequisite to individualized training. These include medication administration and glucagon administration.
Oregon Department of Education (ODE)
Hemophilia Federation of America
Hemophilia.org
Templates
The following templates are modifiable for use by school nurses as it relates to their practice and should be used consistently with Oregon State Board of Nursing, Delegation Laws and local school policy.
Individualized Health Plans
An individualized health plan is the totality of the plan that includes all applicable procedures for students with chronic disease. Because these are intended to be individualized, the attached is an example of a compiled IHP:
Procedures
Procedures also greatly vary by student health status, needs, level of care and type of regimen. The following are sample templates for specific procedures. A complete student assessment should be made to determine appropriate procedures.
Teachers Notification
Self Management
Medication Administration and Self-Medication Agreement
504
About
Authors:
Tiffany Bass
Kathring Carney
Jan Olson
Editorial Reviewer: Ann Occhi
References
- American Society of Hematology. (2023). Bleeding Disorders. https://www.hematology.org/education/patients/bleeding-disorders#:~:text=Bleeding%20disorders%20such%20as%20hemophilia,the%20blood's%20natural%20clotting%20factors.
- Atilla B, Güney-Deniz H. Musculoskeletal treatment in haemophilia. EFORT Open Rev. 2019 Jun 3;4(6):230-239. doi: 10.1302/2058-5241.4.180068. PMID: 31210965; PMCID: PMC6549116.
- Centers for Disease Control and Prevention ( 2022) Hemophilia home care. https://www.cdc.gov/ncbddd/hemophilia/course/overview.html
- Cygan, M., Maier, P., O’Neill, S (2012) The student with a bleeding disorder. https://www.hemophilia.org/sites/default/files/document/files/nurses-guide-chapter-14-student-with-a-bleeding-disorder.pdf
- Gavin, M (. 2021). Hemophilia Factsheet (for Schools). https://kidshealth.org/en/parents/hemophilia-factsheet.html
- Govorov I, Ekelund L, Chaireti R, Elfvinge P, Holmström M, Bremme K, Mints M. (2016) Heavy menstrual bleeding and health-associated quality of life in women with von Willebrand's disease. Exp Ther Med. 2016 May;11(5):1923-1929. doi: 10.3892/etm.2016.3144. Epub 2016 Mar 10. PMID: 27168829; PMCID: PMC4840542.
- Howell C, Scott K, Patel DR. (2017) Sports participation recommendations for patients with bleeding disorders. Transl Pediatr;6(3):174-180. doi: 10.21037/tp.2017.04.07. PMID: 28795008; PMCID: PMC5532193.
- MacDonald, J. (2018)Moving Forward Despite Hemophilia Battle Fatigue. https://hemophilianewstoday.com/columns/hemophilia-battle-fatigue-moving-forward/
- Mayo Clinic ( 2021). Hemophilia. https://www.mayoclinic.org/diseases-conditions/hemophilia/symptoms-causes/syc-20373327.
- Region VII Nursing/Social Work Group (n.d.)Are you Ready to be on Target? Assessing for Readiness for Self-infusion. Nursing-Social WorkGroup https://www.hemophilia.org/sites/default/files/document/files/Assessing-Readiness-for-Self-Infusion.pdf
- Shapiro AD, Donfield SM, Lynn HS, Cool VA, Stehbens JA, Hunsberger SL, Tonetta S, Gomperts ED; Academic Achievement in Children with Hemophilia Study Group. Defining the impact of hemophilia: the Academic Achievement in Children with Hemophilia Study. Pediatrics. 2001 Dec;108(6):E105. doi: 10.1542/peds.108.6.e105. PMID: 11731632.
- Schrijvers LH, Schuurmans MJ, Fischer K. (2016) Promoting self-management and adherence during prophylaxis: evidence-based recommendations for haemophilia professionals. Haemophilia. 22(4):499-506. doi: 10.1111/hae.12904. Epub 2016 Apr 14. PMID: 27075653.
- Steps for Living ( 2020) School Tool Kit For People With Bleeding Disorders.https://stepsforliving.hemophilia.org/resources/next-step-resources